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KMID : 0371320120820040261
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Journal of the Korean Surgical Society
2012 Volume.82 No. 4 p.261 ~ p.265
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Spontaneous aortic rupture in a patient with neurofibromatosis type 1
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Park Yang-Jin
Park Keun-Myoung
Oh Ji-Young
Park Hong-Suk
Kim Jung-Sun
Kim Young-Wook
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Abstract
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Neurofibromatosis type I (NF-1) is a rare autosomal dominant genetic disorder occurring in 1 in 3,000 individuals. Vasculopathy is a rarely reported finding in patients with NF-1. Here, we report a case of recurrent aortic pseudoaneurysm after endovascular aneurysm repair in a 49-year-old male patient with NF-1. On the sixth postoperative day following a successful open surgical repair of an aortic pseudoaneurysm, he developed hemoperitoneum due to a delayed rupture of the mesenteric artery branch. This was treated with endovascular coil embolization. We report the clinical features and histologic findings of this rare vascular disorder with a review of the relevant literature.
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KEYWORD
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Aortic aneurysm, Aortic rupture, Neurofibromatosis 1
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